ASH Clinical News October 2017 | Page 36

Literature Scan Early Evidence Suggests PD-1 Inhibitors May Be Effective in Relapsed/Refractory Mediastinal Gray-Zone Lymphoma Mediastinal gray-zone lymphoma, nodu- lar sclerosis classic Hodgkin lymphoma (cHL), and primary mediastinal B-cell lymphoma have overlapping clinical, histologic, and molecular features, including the frequency of 9p24.1 copy-number alterations associated with susceptibility to immune check- point inhibition. Such alterations occur in approximately 61 percent of patients with mediastinal gray-zone lymphoma, which is typically resis- tant to treatment. In a Letter to the Editor published in the New England Journal of Medicine, Christopher Melani, MD, of the National Cancer Institute in Bethesda, Maryland, and colleagues noted “recent findings indicate that mediastinal gray-zone lymphoma may be more closely related to cHL than to primary mediastinal B-cell lymphoma” and therefore may respond to immune checkpoint inhibition. Dr. Melani described three case studies that demonstrate “early evidence for using PD-1 inhibition [with agents like nivolumab and pembrolizumab] in relapsed or refractory mediastinal gray-zone lymphoma.” • Case 1: An 18-year-old woman with mediastinal gray-zone lymphoma (confirmed after a biopsy of a mediastinal mass showed an immunophenotype intermediate between diffuse large B-cell lymphoma [DLBCL] and cHL, which was positive for CD20, CD30, and CD15) experienced a partial response (PR) to dose- adjusted etoposide, doxorubicin, and cyclophosphamide with vincristine and prednisone plus rituximab (DA-EPOCH-R). However, six weeks after salvage radiotherapy, her disease progressed. She was then treated with pembrolizumab and had a complete metabolic response (defined as normalization of an abnormal positron emission tomography scan). After 235 days of treatment, she underwent allogeneic hematopoietic cell transplantation. Fluorescence in situ hybridization (FISH) detected rearrangement of the genes encoding the PD-1 and PD-2 ligands. • Case 2: A 76-year-old man with mediastinal gray-zone 34 ASH Clinical News lymphoma (confirmed after a biopsy of a subcarinal mass showed DLBCL with an immunophenotype of cHL, which was positive for CD30 and PAX5 and negative for CD10, CD20, and CD15) also experienced a PR to DA-EPOCH-R, but his disease subsequently progressed. After treatment with pembrolizumab, he had a complete metabolic response and continues to be in remission after 381 days of treatment. FISH detected ADYNOVATE ® is FDA approved for patients of all ages with Hemophilia A PROVEN PROPHYLAXIS + SIMPLE, * TWICE-WEEKLY L Y DOSING LY D OSING SCHEDULE = moments THEIR WAY * ADYNOVATE allows patients to infuse on the same 2 days every week. ADYNOVATE [Antihemophilic Factor (Recombinant), PEGylated] Important Information Indications ADYNOVATE, Antihemophilic Factor (Recombinant), PEGylated, is a human antihemophilic factor indicated in children and adults with hemophilia A (congenital factor VIII deficiency) for: • On-demand treatment and control of bleeding episodes • Perioperative management • Routine prophylaxis to reduce the frequency of bleeding episodes Limitation of Use ADYNOVATE is not indicated for the treatment of von Willebrand disease. DETAILED IMPORTANT RISK INFORMATION CONTRAINDICATIONS ADYNOVATE is contraindicated in patients who have had prior anaphylactic reaction to ADYNOVATE, to the parent molecule (ADVATE [Antihemophilic Factor (Recombinant)]), mouse or hamster protein, or excipients of ADYNOVATE (e.g. Tris, mannitol, trehalose, glutathione, and/or polysorbate 80). WARNINGS & PRECAUTIONS Hypersensitivity Reactions Hypersensitivity reactions are possible with ADYNOVATE. Allergic-type hypersensitivity reactions, including anaphylaxis, have been reported with other recombinant antihemophilic factor VIII products, including the parent molecule, ADVATE. Early signs of hypersensitivity reactions that can progress to anaphylaxis may include angioedema, chest tightness, dyspnea, wheezing, urticaria, and pruritus. Immediately discontinue administration and initiate appropriate treatment if hypersensitivity reactions occur.