ASH Clinical News ACN_4.2_FULL_ISSUE | Page 18

Data Stream Facts and figures from research presented at the 2017 ASH Annual Meeting Making CLL More Chronic Hammering Sickling Treatment with the BCL2 inhibitor venetoclax and rituximab (VR) more than doubled the likelihood that patients with relapsed/refractory chronic lymphocytic leukemia (CLL) survived to two years without disease progression, compared with bendamustine and rituximab (BR). Teenagers with sickle cell disease (SCD) may have a new treatment option that addresses the underlying cause of the disease, according to preliminary results from a trial of voxelotor. “What sets this drug apart is that it was designed spe- cifically for SCD,” said lead study author Carolyn C. Hoppe, MD. “This is one of the first drugs that intentionally targets the fundamental mechanism of SCD.” Among 389 patients randomized to receive either VR or the standard chemo- immunotherapeutic regimen: Progression-free survival 84.9 % VR Group 55 % Of the patients (ages 12-17 years) with SCD who received at least 16 weeks of voxelotor treatment, 55% (n=6/11) experienced a >1 g/dL increase in hemoglobin. Voxelotor also appeared to improve patients’ quality of life: 83% saw improvement in total severity score, including 42% who experienced no symptoms. 83 % 42 % Safety and tolerability data were reassuring, the authors noted, but results will need to be confirmed in larger, randomized trials. Source: Hoppe CC, Inati AC, Brown C, et al. Initial results from a cohort in a phase 2a study (GBT440-007) evaluating adolescents with sickle cell disease treated with multiple doses of GBT440, a HbS polymerization inhibitor. Abstract #689. Presented at the 2017 American Society of Hematology Annual Meeting, December 11, 2017; Atlanta, GA. 36.3 % BR Group A Game-Changer for aTTP Minimal Residual Disease Clearance 83.5 % VR Group 23.1 % BR Group 0% 20% 40% 60% 80% 100% “This is the first randomized trial comparing any of the new agents targeted to treat CLL against a standard chemoimmunotherapy program,” said lead study author John Seymour, MBBS, PhD, adding that the results “suggest that venetoclax should replace chemotherapy for relapsed/refractory CLL.” The researchers are continuing to monitor participants to assess long-term safety, survival, and disease progression. Source: Seymour JF, Kipps TJ, Eichhorst BF, et al. Venetoclax plus rituximab is superior to bendamustine plus rituximab in patients with relapsed/refractory chronic lymphocytic leukemia - results from pre-planned interim analysis of the randomized phase 3 Murano study. Abstract LBA-2. Presented at the 2017 American Society of Hematology Annual Meeting, December 12, 2017; Atlanta, GA. 16 ASH Clinical News In a phase III trial, treatment with the anti–von Willebrand factor antibody caplacizumab reduced the immediate risks and prevented organ damage associated with acquired thrombocytopenic purpura (aTTP). “This is a real game cha